Abstract

SURGICAL MANAGEMENT OF PAGET’S DISEASE OF THE VULVA: A CASE REPORT

Abderrahim Siati*, Taher Berrada, Aziz Baidada and Aicha Kharbach

ABSTRACT

Extra-mammary Paget disease (EMPD) is one of the rare neoplastic conditions of the skin that accounts for less than 1% of the vulvar malignancies. The condition typically presents as a red, velvety, pruritic skin rash of the vulva region which mimics a multitude of other, more common conditions in postmenopausal women. Well-established guidelines for diagnosis and management are not available for this rare condition. As a result, vulvar Paget's disease is frequently misdiagnosed, and could be associated with multifocal neoplasms. The current gold standard for the treatment of vulvar EMPD is surgical excision. Our patient is a 64-year-old postmenopausal woman with the complaint of itching of two years duration. She was diagnosed with EMPD on incisional biopsy and treated with only surgery at our centre. No recurrence was seen during two years after treatment with disappearance of pain and improved quality of life.

Keywords: Paget’s disease, Vulva, Surgical treatment.