Abstract

ASSESSMENT OF QUALITY OF LIFE AND FUNCTIONAL DISABILITY AMONG HEMOPHILIA A PATIENTS IN MAHARASHTRA, INDIA

Rucha M., Gaurav D., Neha K. and Hrishikesh G.*

ABSTRACT

Hemophilia is characterized by spontaneous and post-traumatic bleeding and its complications in joints and muscles leads to severe pain, severe joint damage, disability, and a dramatic impairment of quality of life (QOL). The purpose of the study is to access the QOL and to determine the functional disability affecting the individuals with haemophilia A. 102 male patients of hemophilia A of age > 5 years and on clotting factor concentrate treatment (on-demand protocol) were included in the study. QOL was assessed with SF-36 questionnaire which includes 36 questions measuring physical and mental health with respect to eight health domains. Functional evaluation was done by World Federation of Hemophilia (WFH) approved Gilbert scoring system. Pearson Correlation explored the association between age of diagnosis, functional disability and QOL. In our study, QOL of hemophilia A patients was seems to be satisfactory and negative correlation was found between the quality of life and functional disability in hemophilic patients.

Keywords: Hemophilia, Quality of life, Functional Disability, SF-36, Gilbert Scale.